Collagen VI Antibody

Cat no: 251203

Supplier: ABBIOTEC

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Description
Additional Information

Collagen VI acts as a cell-binding protein. Collagen VI is a trimer composed of three different chains: alpha-1(VI), alpha-2(VI), and alpha-3(VI) or alpha-5(VI) or alpha-6(VI). Defects in collagen VI are a cause of Bethlem myopathy (BM). BM is a rare autosomal dominant pro, Xenopus/Amphibian,imal myopathy characterized by early childhood onset (complete penetrance by the age of 5) and joint contractures most frequently affecting the elbows and ankles.

Catalogue number:	251203
Reactivities:	Human, Mouse, Bovine, Canine, Chicken/Bird, Porcine, Rabbit
Applications:	Immunohistochemistry
Size:	0.1 mg
Accession:	P12109
Antigen:	KLH-conjugated synthetic peptide encompassing a sequence within the center region of human collagen VI.
Format:	Each vial contains 0.1 mg IgG in 0.1 ml (1 mg/ml) of PBS pH7.4 with 0.09% sodium azide. Antibody was purified by Protein-G affinity chromatography.
P type:	Rabbit Polyclonal Antibody
Isotype:	Rabbit Ig
Additional info:	Collagen VI; Collagen Type VI; Collagen alpha-1(VI) chain; COL6A1