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CPT2 (Carnitine Palmitoyltransferase 2, Carnitine O-palmitoyltransferase, OTTHUMP00000010493, CPTASE, CPT1, Carnitine Palmitoyltransferase II, CPT2)

CPT2 (Carnitine Palmitoyltransferase 2, Carnitine O-palmitoyltransferase, OTTHUMP00000010493, CPTASE, CPT1, Carnitine Palmitoyltransferase II, CPT2)

Cat no: C1385-50C

Supplier: United States Biological
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The protein encoded by this gene is a nuclear protein which is transported to the mitochondrial inner membrane. Together with carnitine palmitoyltransferase I, the encoded protein oxidizes long-chain fatty acids in the mitochondria. Defects in this gene are associated with mitochondrial long-chain fatty-acid (LCFA) oxidation disorders. Applications: Suitable for use in ELISA and Western Blot. Other applications have not been tested. Recommended Dilutions: Peptide ELISA Titer: 1:4000 Western Blot: 1-3ug/ml ~70kD and 37kD in Human Liver lysates. These bands correspond to earlier findings with different antibodies from other commercial sources.This protein has a calculated MW of 73.8kD according to NP_000089.1. Optimal dilutions to be determined by the researcher. Storage and Stability: May be stored at 4 degrees C for short-term only. Aliquot to avoid repeated freezing and thawing. Store at -20 degrees C. Aliquots are stable for at least 12 months. For maximum recovery of product, centrifuge the original vial after thawing and prior to removing the cap.
Catalogue number: C1385-50C
Reactivities: Human
Hosts: Goat
Applications: ELISA, Western Blot
Size: 100ug
Form: Supplied as a liquid in Tris saline, pH 7.3, 0.5% BSA, 0.02% sodium azide.
P type: Pab
Isotype: IgG
Purity: Purified by peptide affinity chromatography.
Alternative names: carnitine O-palmitoyltransferase, OTTHUMP00000010493, CPTASE, CPT1, carnitine palmitoyltransferase II, CPT2
References: 1. Isackson PJ, Bennett MJ, Lichter-Konecki U, Willis M, Nyhan WL, Sutton VR, Tein I, Vladutiu GD, CPT2 gene mutations resulting in lethal neonatal or severe infantile carnitine palmitoyltransferase II deficiency. Molecular genetics and metabolism 2008 Aug 94 (4): 422-7.
Additional info: Recognizes human CPT2.

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