Quick Search
Products Dysferlin (Dystrophy-associated Fer-1-like Protein, DYSF, Fer-1-like Protein 1, FER1L1, LGMD2B, MMD1)
| Catalogue number: | D9904-60F |
| Reactivities: | Human |
| Hosts: | Mouse |
| Applications: | Immunohistochemistry, Western Blot |
| Size: | 1ml |
| Form: | Supplied as a lyophilized powder in PBS, 1% BSA, 15mM sodium azide. Reconstitute with 1ml dH2O. |
| P type: | Mab |
| Isotype: | IgG2b,k |
| Purity: | Supernatant |
| Alternative names: | Dysferlin, Limb Girdle Muscular Dystrophy 2B (Autosomal Recessive) |
| References: | 1.Anderson LVB, Davison K, Moss J A, et al.. Dysferlin is a plasma membrane protein and is expressed early in human development. Human Molecular Genetics 8:855-861 (1999). 2.Anderson L V B and Davison K. Multiplex western blotting system for the analysis of muscular dystrophy proteins. American Journal of Pathology 154(4):1017-1022 (1999). 3.Bittner R E, Anderson L V B, Burkhardt E, et al.. Dysferlin deletion in SJL mice (SJL-Dysf) defines a natural model for limb girdle muscular dystrophy 2B. Nature Genetics 23:141-142 (1999). 4.Weiler T, Bashir R, Anderson L V B, et al.. Identical mutations in patients with limb girdle muscular dystrophy type 2B or miyoshi myopathy suggests a role for modifier gene(s). Human Molecular Genetics 8:871-877 (1999). |
| Additional info: | Recognizes human Dysferlin. |
Get the Best Promotions
