Fibrillin-1 Antibody

Cat no: 251526

Supplier: ABBIOTEC

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Description
Additional Information

Fibrillins are structural components of 10-12 nm e, Xenopus/Amphibian,tracellular calcium-binding microfibrils, which occur either in association with elastin or in elastin-free bundles. Fibrillin-1-containing microfibrils provide long-term force bearing structural support. Defects in fibrillin-1 are a cause of Marfan syndrome (MFS), an autosomal dominant disorder that affects the skeletal, ocular, and cardiovascular systems. A wide variety of skeletal abnormalities occurs with MFS, including scoliosis, chest wall deformity, tall stature, abnormal joint mobility.

Catalogue number:	251526
Reactivities:	Human, Mouse, Rabbit
Applications:	Immunohistochemistry
Size:	0.1 mg
Accession:	P35555
Antigen:	KLH-conjugated synthetic peptide encompassing a sequence within the N-term region of human fibrillin-1.
Format:	Each vial contains 0.1 mg IgG in 0.1 ml (1 mg/ml) of PBS pH7.4 with 0.09% sodium azide. Antibody was purified by Protein-G affinity chromatography.
P type:	Rabbit Polyclonal Antibody
Isotype:	Rabbit Ig
Additional info:	FBN1; Fibrillin-1; FBN